My grandson was just diagnosed with Ebsteins Anomaly is it dangerous,and what can be done for it?

Answer 1

Ebstein's Anomaly
What It Is

Ebstein's anomaly, also called Ebstein's malformation, is a heart defect in which the tricuspid valve is abnormally formed. The tricuspid valve normally has three "flaps" or leaflets. In Ebstein's anomaly, one or two of the three leaflets are stuck to the wall of the heart and don't move normally. Often there's also a hole in the wall between the atria, the heart's two upper chambers. This hole is called an atrial septal defect or ASD. (See the section on Atrial Septal Defect.) Because the tricuspid valve is malformed in Ebstein's anomaly, it often doesn't work properly and may leak. If the valve leaks, some of the blood pumped by the right ventricle goes backwards through the valve with each heartbeat.

Surgical Treatment

Ebstein's anomaly is mild in most adults who have it, so they don't need surgery. However sometimes the tricuspid valve leaks severely enough to result in heart failure or cyanosis (see the Glossary). Then surgery may be required.

Several different operations have been used in patients with Ebstein's anomaly. The most common involves a repair of the tricuspid valve. The valve can't be made normal, but often surgery significantly reduces the amount of leaking. If there's an ASD, it's usually closed at the same time. In some cases the tricuspid valve can't be adequately repaired. Then it's replaced with an artificial valve.

Ongoing Care

Medical

People with Ebstein's anomaly should receive continued care from a cardiologist with expertise in congenital heart defects. Besides getting information from routine exams, the cardiologist may use tests such as electrocardiograms, Holter monitor and echocardiograms. (See the Glossary.)

Activity Restrictions

Being physically active is good for your cardiovascular system, so stay active. (See the section on Physical Activity). If valve leakage is mild and tests show no abnormal heart rhythms, you can usually participate in most sports. Your cardiologist may recommend avoiding certain intense competitive sports. Ask your cardiologist which activities are right for you.

Endocarditis Prevention

You may need antibiotics before certain dental or surgical procedures to prevent endocarditis. (See the section on Endocarditis.)