what is von wilderbrandt's disease?

Answer 1

Hi Hunny, check out the haemophili society web site http://www.haemophilia.org.uk/ My son ha hamophilia B Mild but before he was diagnosed they thought it could have been Von Willebrand's. The site is great and hey should be able to tell you what you needed to know ok x x x x

Answer 2

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"Information is Power"

Providing Information on von Willebrand's Disease

and Links to von Willebrand's & Hemophilia Web Pages

Go To Personal Information
What Is Von Willebrand's Disease?

Von Willebrand's Disease (vWD) is not a disease at all, but the most common genetic disorder in the world (classic hemophilia is more well known due to its connection with the royal families of Europe). In fact, vWD is 100 times more common than classic hemophilia! It was discovered by a Finnish doctor in the 1920s, who named it after himself and called it a disease. Later, Dr. von Willebrand discovered in truth that the illness was linked to a missing blood factor, which assists with the clotting of blood. He named the factor after himself as well - von Willebrand's Factor (vWF). The disorder is not sex linked (autosomal), meaning that both men and women can have it, but some can be carriers only and not manifest any of the symptoms. VWD occurs when the body makes either inferior vWF or none at all. Other blood factors can be short-changed as well. Generally, vWD is divided into three types: Type I (mild), Type II (Medium) and Type III (severe). The lower the type, the less the symptoms will occur and the less strenuous they will be.



What Are the Symptoms?

Usually, vWD shows itself by spontaneous hemmorhages under the skin, prolonged and/or easy bruising, and prolonged bleeding from even small cuts. Most internal hemmorhages occur in crisis joints - a joint (knee, elbow, etc.) that usually will be the first to bleed. Time for the bruising and bleeding to stop depends on the amount and quality of vWF in the blood system. Rough sports without adequate protection are not advised. Take care when visiting the dentist. And don't become the glass-eating geek at the circus.



What Are the Treatments?

Types I and II usually are treated with desmopressin, also known as DDAVP, a nasal spray, while Type III has a variety of blood factor products that put good quality vWF into the bloodstream, such as Kogen, Humate-P and Kogate. There is no guarantee that having a certain type of vWD will automatically call for the usual treatment; you must see a hemotologist to be sure of your type, and then may have to carefully try several products to find the correct one for you. The recent medical advances make sure that products are much more clear of blood-borne infections than when cryoprecipitate was the only treatment.



Where Can I Find More Information?

The best national source for information is the National Hemophilia Foundation, which can give more detailed information than this site. They can send you the appropriate information on von Willebrand's Disease, plus information on any other blood disorders, local chapters and caregivers.

Answer 3

It looks to be something that affects dobermans. I went on the internet and typed it into a search and there are several links available that include information. Each one that I looked at had references to dogs. Check it out. I used Yahoo search engine but I'm sure google, jeeves or any of the others will be just as good.

Answer 4

To answer that without getting too technical, it's an inherited clotting disorder where a protein necessary for proper function of the platelets is not made correctly. The practical upshot is increased bleeding, and often bleeding from things that wouldn't normally cause it, such as brushing your teeth.

Answer 5

It is a congenital bleeding disorder, which manifests itself at a very early age. Symptoms are excessive nosebleed and bruising.

Answer 6

look the disease up on the internet

Answer 7

neurofibromatosis